The description of the eight cases Goldenhar`syndrome. Of these five cases are typical: hemilesion face hypoplasia, facial muscles and facial bones, makrostomiya, open bite, arkovidnoe sky, cleft lip and palate. Colobomas of the upper eyelid, ptosis, microphthalmia, strabismus. Deformations of the ears, middle ear abnormalities, deafness. Malformation of the cervical spine and urinary tract. One case with multiple anomalies of face, spine shows a more pronounced clinical symptoms of the syndrome. In two cases, described an atypical syndrome: a bilateral lesion of ears and pronounced changes in the middle and inner ear in unilateral lesion of the person, including cleft lip and palate.